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Hydrocephalus

Normal CSF Circulation

  • CSF is an ultrafiltrate of the plasma
  • Secreted by the choroid plexuses of the third, fourth and lateral ventricles
  • Total volume of CSF is approximately 150 ml
  • Approximately 500 ml of CSF is produced each day
  • CSF circulates from ventricles into subarachnoid space
  • Absorbed by the arachnoid granulations around the superior sagital sinus
  • In health rate of production equals rate of absorption
  • CSF pressure is usually 10-15 cm water

Causes of hydrocephalus

  • Hydrocephalus is characterised by dilated cerebral ventricles
  • Intraventricular pressure can be normal or raised
  • Usually arises due to interruption to the normal flow of CSF
  • Two main types of hydrocephalus are recognised
    • Communicating hydrocephalus
    • Non-communicating hydrocephalus

Communicating hydrocephalus

  • Obstruction is in the subarachnoid space
  • Results in dilatation of the entire ventricular system
  • Causes include:
    • Meningitis
    • Intraventricular haemorrhage
    • Congenital absence of the arachnoid granulations
    • Arnold-Chiari malformation
    • Encephalocele
    • Choroid plexus papilloma

Non-communicating hydrocephalus

  • Obstruction is within the ventricular system
  • Usually results from congenital or neoplastic lesions
  • Causes include:
    • Aqueduct stenosis
    • Atresia of the foramina of Magendie and Luschka
    • Ventriculitis
    • Intraventricular tumours
    • Dandy-Walker syndrome

Clinical Features

  • May be diagnosed on antenatal ultrasound
  • Postnatal diagnosis depends on the rate of progression of the hydrocephalus
  • Acute hydrocephalus presents with features of raised ICP
  • Features include headache, vomiting, drowsiness and papilloedema
  • Chronic hydrocephalus presents with:
    • Enlarging head circumference
    • 'Sun-set' eyes
    • Tense fontanelle
    • Cranial nerve palsies
  • Diagnosis and causes can be confirmed by CT or MRI scan

Management

  • Established hydrocephalus requires CSF drainage
  • Temporary CSF drainage can be achieved with an external ventricular drain
  • Permanent CSF drainage is carried out by diversion of CSF  into a body cavity
  • Possible routes included
    • Peritoneum
    • Right atrium
    • Pleural cavity
  • Most shunts have several components including
    • Proximal catheter
    • One way valve
    • CSF reservoir
    • Distal catheter
  • Complications of ventricular peritoneal shunts
    • Infection
    • Blockage
    • Overdrainage
    • Disconnection
    • Intracranial haemorrhage
    • Ascites

Bibliography

Li V.  Methods and complications in surgical cerebrospinal fluid shunting.  Neurosurg Clin North Am 2001;  12:  685-693.

Lo P,  Drake J M.  Shunt malfunctions.  Neurosurg Clin North Am 2001:  12:  695-701.

Meyer P G,  Ducrocq S,  Carli P.  Pediatric neurologic emergencies.  Curr Opin Crit Care 2001;  7:  81-87.

Siddique M S,  Mendelow A D.  Surgical treatment of intracerebral haemorrhage.  Br Med Bull 2000;  56:  444-456.

 

 
 

Last updated: 05 January 2008

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